Pediatr. praxi. 2016;17(4):252-255 | DOI: 10.36290/ped.2016.058

Recurrent spontaneous pneumothorax in adolescent

MUDr.Kateřina Navrátilová¹, MUDr.Kamila Michálková², MUDr.Josef Chudáček, Ph.D.³, prof.MUDr.František Kopřiva, CSc.¹

¹ Dětská klinika LF UP a FN v Olomouci

² Radiologická klinika LF UP a FN v Olomouci

³ 1. chirurgická klinika LF UP a FN v Olomouci

This case report describes the 14 year old adolescent, who was diagnosed with Marfan syndrome at the age of 12 years. This

patient was admitted to our hospital with present complains of breathlessness, cough, chest pain and vertigo. The subsequent

investigations led to the diagnosis of an unilateral spontaneous pneumothorax on the right, which was resolved through an

active drainage. The patient was readmitted three days later with a new ipsilateral pneumothorax, a computerised tomography

has shown subpleural bullae in the right lung. According to the decision of pneumologist surgical resection of identified bullae

and pleurodesis were performed, which should be able to prevent the recurrent pneumothorax in identical localization. This case

report highlights the importance of a correct therapeutic approach to the spontaneous pneumothorax, describes common risks

of spontaneuos pnemothorax in patients wtih Marfan syndrome, diagnostic criteria of Marfan syndrome, last but not least the

conditions related to Marfan syndrome, e.g. pectus excavatum or scoliosis and the ways of its possible prevention.

Keywords: spontaneous pneumothorax, Marfan syndrome, pectus excavatum, bullosus diseases

Published: October 1, 2016  Show citation