Pediatr. praxi. 2020;21(5):374-376 | DOI: 10.36290/ped.2020.077
Dextrocardia in a child with left‑sided poland syndrome
- 1 Ústav molekulární a translační medicíny LF UP Olomouc
- 2 Dětská klinika LF UP a FN v Olomouci
- 3 Radiologická klinika LF UP a FN v Olomouci
Poland syndrome (PS) is a rare congenital anomaly accompanied by the unilateral absence of the pectoralis major, and the ipsilateral chest-wall and upper-limb deformity. The combination of PS and dextrocardia is very uncommon, only 20 cases having been published until now. If coexistence of dextrocardia in PS is present, it is almost always associated with left chest deformities. We present a nine-month-old infant with left-sided PS associated with isolated dextrocardia and partial agenesis of the 3rd and 4th left ribs.
Keywords: left‑sided Poland syndrome, dextrocardia, 3rd and 4th partial rib agensis, infant.
Published: October 16, 2020 Show citation
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